This formation of the platelet plug is called primary hemostasis.

程即初期止。

The formation of this platelet plug is called primary hemostasis.

被称为初级止程。

The formation of the platelet plug is called primary hemostasis.

小板栓子的形成叫做期止。

This is because the process called hemostasis, literally meaning to stop the flow of blood, is impaired.

是因为友病患者的止程受损，即其功能出现障碍。

Normally, protein C and protein S are 2 of many proteins or enzymes that regulate the complex process called hemostasis.

通常，蛋白C和蛋白S是能调止复杂程的许多蛋白和酶类的其中两种。

The main role of protein C and protein S is to prevent excess coagulation, or fibrin formation, during secondary hemostasis.

蛋白C和蛋白S的主要作用是在二期止时防止度（即纤维蛋白形成多）。

People who suffer from disorders related to hemostasis may have trouble with unwanted clotting, or the inability to form clots.

患有与止相关疾病的人可能会有不必要的无法形成块的问题。

The second factor is a state of hypercoagulation, where altered amounts of clotting factors increase primary or secondary hemostasis.

第二个因素是高状态，高状态下因子数量增多，会增强初期二期。

So, it has a whole system in place to prevent you from losing too much of it, through a process known as hemostasis.

所以，它有个完整的系统来防止你失去太多，通个被称为止的程。

Now, a mimic of hemophilia A is von Willebrand disease, which is an inherited problem with primary hemostasis caused by a deficiency of von Willebrand factor.

还有种类友病A，即管性友病，是种遗传性的初级止障碍，由管性友病因子（vWF）缺乏引起。

So these steps leading up to fibrin reinforcement of the platelet plug make up the process called secondary hemostasis and results in a hard clot at the site of the injury.

加强小板栓强度的程即为二期止，最终使得伤口上的栓很牢固。

In the family of disorders known as hemophilia, a patient can usually complete the first two steps of hemostasis just fine, but they can't make an effective fibrin clot.

在被称为友病的疾病家族中，病人通常可以很好地完成止的前两个步骤，但是他们不能制造有效的纤维蛋白块。

In most cases of hemophilia there is a decrease in the amount or function of one or more of the clotting factors that makes secondary hemostasis less effective and allows more bleeding to occur.

在大多数友病中，都有种多种因子在数量上减少功能上减弱，使次级止程的功效下降，而出更多。

To make things worse, as the clots are broken down through fibrinolysis, fibrin degradation products are released into the circulation and these interfere with platelet aggregation and clot formation, making hemostasis even more difficult.

更糟的是，当块通纤溶崩解时，纤维蛋白降解产物释放入液循环，干扰小板聚集和块形成，导致更加困难。